ABSTRACT
Los hidrocistomas apocrinos son lesiones quísticas benignas. Clínicamente se caracterizan por ser nódulos quísticos claros o traslucidos, solitarios, en forma de cúpula, con superficie lisa. En la mayoría de los casos la localización suele ser alrededor del ojo, particularmente lateral al canto externo. Suelen ser asintomáticos, de crecimiento lento pudiendo llegar a 10 mm de diámetro o más. Presentamos un caso de un paciente con un hidrocistoma apocrino variante pigmentada.
Apocrine hydrocystomas are benign cystic lesions, clinically characterized by being clear or translucent cystic nodules, solitary, domeshaped, with a smooth surface. In most cases the location is usually around the eye, particularly lateral to the outer edge. They are usually asymptomatic, slow growing and can reach 10 mm in diameter or more. We present a case of a patient with a pigmented variant apocrine hydrocystom
Subject(s)
Humans , Middle Aged , Sweat Gland Neoplasms/diagnosis , Hidrocystoma/diagnosis , Dermoscopy/methods , Apocrine Glands , Sweat Gland Neoplasms/pathology , Hidrocystoma/pathologyABSTRACT
ABSTRACT The authors report the first case in Brazilian literature of orbital apocrine hidrocystoma with immunohistochemistry confirmation. The tumor had been growing slowly and progressively, there was no history of impaired vision, diplopia, watering, discharge, or prior trauma. There was no proptosis and extraocular mobility was normal. The radiologic study by orbital computerized tomography revealed an extraconal nodule, with partially defined limits, with cystic and solid areas in the superomedial right orbit. An anterior orbitotomy, with full excision of the tumor was performed. A histopathology examination revealed apocrine hidrocystoma and immunohistochemistry confirmed the diagnosis. After surgery, the patient had total remission of symptoms.
RESUMO Os autores relatam o primeiro caso de hidrocistoma apócrino orbitário com confirmação imunohistoquímica. O tumor apresentou crescimento lento e progressivo, sem relato de baixa de acuidade visual, diplopia, epífora, secreção ou trauma prévio. Não houve proptose ou alteração da motilidade extraocular. O exame de imagem por tomografia computadorizada da órbita revelou uma lesão nodular, extraconal, de limites imprecisos, com áreas císticas e sólidas no seu interior, na região súpero-medial de órbita direita. O paciente foi submetido à orbitotomia por via anterior, com exérese integral da tumoração. O exame histopatológico revelou o diagnóstico de hidrocistoma apócrino e a imunohistoquímica confirmou o diagnóstico. Após a cirurgia, o paciente teve regressão total dos sintomas.
Subject(s)
Humans , Female , Middle Aged , Sweat Gland Neoplasms/diagnosis , Orbital Neoplasms/diagnosis , Immunohistochemistry/methods , Hidrocystoma/diagnosis , Apocrine Glands/pathology , Sweat Gland Neoplasms/surgery , Sweat Gland Neoplasms/pathology , Biopsy , Orbital Neoplasms/surgery , Orbital Neoplasms/pathology , Biomarkers, Tumor , Tomography, X-Ray Computed , Hidrocystoma/surgery , Hidrocystoma/pathology , Eyelids/pathologySubject(s)
Humans , Male , Middle Aged , Hidrocystoma/surgery , Laser Therapy , Skin Neoplasms/surgery , Sebaceous Gland Neoplasms/surgery , Biopsy , Diagnosis, Differential , Hidrocystoma/diagnosis , Hidrocystoma/pathology , Skin Neoplasms/diagnosis , Skin Neoplasms/pathology , Sebaceous Gland Neoplasms/diagnosis , Sebaceous Gland Neoplasms/pathology , Treatment OutcomeABSTRACT
Existen varios tipos de lesiones quísticas de la órbita, las cuales presentan características ecográficas comunes como forma redonda u oval, superficie bien delimitada de bordes definidos, y ausencia de vascularidad interna. Dichas lesiones son habitualmente fáciles de diferenciar de los tumores sólidos.
Subject(s)
Orbital Diseases/diagnosis , Teratoma/diagnosis , Hidrocystoma/diagnosis , Dermoid Cyst/diagnosis , Mucocele/diagnosis , Ultrasonography , Orbit/pathologyABSTRACT
Se presenta una paciente de 28 años de edad con hidrocistomas ecrinos múltiples localizados en la cara anterior de ambos antebrazos, relacionada su aparicicón con la exposición a una fuente de calor. Se efectúa microscopía óptica y electrónica así como estudio inmunohistoquímico de las lesiones y se comentan las características clínicas y posibilidades terapéuticas de esta afección